prenatal diagnosis of tuberous sclerosis by fetal echocardiography with an unusual clinical course after birth

نویسندگان

maryam moradian rajaie cardiovascular, medical and research center, iran university of medical sciences, tehran, ir iran; rajaie cardiovascular, medical and research center, iran university of medical sciences, tehran, ir iran , +98-2123922170

mohammad dalili rajaie cardiovascular, medical and research center, iran university of medical sciences, tehran, ir iran

mahmood merajie rajaie cardiovascular, medical and research center, iran university of medical sciences, tehran, ir iran

چکیده

conclusions this case report underscores the role of fetal echocardiography in the prenatal diagnosis of cardiac disease and illustrates rhabdomyomas in a tuberous sclerosis patient. rhabdomyomas are histologically benign; however, they may cause severe arrhythmia even when they are regressing. case presentation our tuberous sclerosis patient developed arrhythmia unexpectedly while his tumors were in regression, presenting a challenge to us as to whether or not opt for surgery. introduction the cardiac outcome in tuberous sclerosis patients is usually favorable, and cerebral manifestations determine the ultimate prognosis in these patients.

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عنوان ژورنال:
archives of cardiovascular imaging

جلد ۱، شماره ۲، صفحات ۸۳-۵

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